Behçet syndrome and Crohn’s disease – what are the differences?

  • Bernardo Baptista Internal Medicine Department, Hospital da Luz, Lisbon, Portugal
  • Natália Marto Internal Medicine Department, Hospital da Luz, Lisbon, Portugal
  • João Galaz Tavares Internal Medicine Department, Hospital da Luz, Lisbon, Portugal
  • Alexandra Bayão Horta Internal Medicine Department, Hospital da Luz, Lisbon, Portugal
  • Diogo Cunha Sá ascular Surgery Department, Hospital da Luz, Lisbon, Portugal
  • Gonçalo Gerardo Pathology Department, Hospital da Luz, Lisbon, Portugal
  • Manuela Mafra Pathology Department, Hospital da Luz, Lisbon, Portugal

Keywords

Behçet syndrome, terminal ileitis, deep venous thrombosis, aneurysm, Crohn’s disease

Abstract

Behçet syndrome (BS) is a variable vessel vasculitis that has pleiotropic manifestations. A 43-year-old male with a previous diagnosis of Crohn’s disease (CD) presented with deep venous thrombosis and bilateral superficial femoral artery aneurysms. A diagnosis of BS was made, and the patient was treated aggressively with immunosuppressive therapy and bilateral bypass surgery, attaining a favourable outcome. CD has many features that overlap with BS, and it may be challenging to distinguish between these two conditions, as our case illustrates. Nonetheless, the combination of venous thrombosis and arterial aneurysms should point the clinician towards a diagnosis of BS.

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  • Published: 2019-03-01

    Issue: Vol 6 No 3 (view)

    Section: Articles

    How to cite:
    Baptista, B., Marto, N., Tavares, J., Horta, A., Sá, D., Gerardo, G., & Mafra, M. (2019). Behçet syndrome and Crohn’s disease – what are the differences?. European Journal of Case Reports in Internal Medicine, 6(3). https://doi.org/https://doi.org/10.12890/2019_001044