Cutaneous Angiosarcoma in an Unusual Location and Without Predisposing Factors

  • Ana Oliveira Monteiro Department of Internal Medicine, Centro Hospitalar Universitário de São João, Porto, Portugal
  • Inês Branco Ferreira Department of Internal Medicine, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • Artur César Department of Dermatology and Venereology, Centro Hospitalar de Vila Nova de Gaia/Espinho, Porto, Portugal
  • Alberto Mota Department of Dermatology and Venereology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S.João, Porto, Portugal
  • Jorge Pinheiro Department of Pathology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • José Manuel Lopes Department of Pathology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • M Teresa Cardoso Department of Internal Medicine, Centro Hospitalar Universitário de S. João, Porto, Portugal

Keywords

Cutaneous angiosarcoma, lower limbs, predisposing factors, immunohistochemistry

Abstract

Cutaneous angiosarcoma is a rare, highly malignant tumour of vascular endothelial origin. It usually arises in the skin and superficial soft tissue, mostly on the head and neck. It presents as a variety of lesions, and so is considered a great mimicker, leading to a delay in diagnosis and evidencing the importance of biopsy with immunohistochemistry confirmation. There are few reports of extremity involvement in patients with pre-existing chronic lymphoedema, or exposure to radiation therapy. We report the case of an 82-year-old woman with lower limb extensive cutaneous involvement, distant metastatic disease, and poor therapy response. Its rare location without predisposing factors highlights the need to raise awareness about this disease

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Published: 2020-09-25

Issue: LATEST ONLINE (view)

Section: Articles

How to cite:
1.
Monteiro AO, Branco Ferreira I, César A, Mota A, Pinheiro J, Manuel Lopes J, Cardoso MT. Cutaneous Angiosarcoma in an Unusual Location and Without Predisposing Factors. EJCRIM [Internet]. 2020Sep.25 [cited 2020Oct.24];20. Available from: https://www.ejcrim.com/index.php/EJCRIM/article/view/1939