Ruptured Sinus of Valsalva Aneurysm Causing Aorto–Atrial Fistula and Acute Heart Failure: A Rare Encounter
  • Zafar Ali
    University of Kansas Medical Center, Kansas City, KS, USA
  • Talal Asif
    John H. Stroger, Jr. Hospital of Cook County, Chicago, IL, USA
  • Justin Sheehy
    University of Missouri–Kansas City, Kansas City, MO, USA
  • Dany Jacob
    University of Missouri–Kansas City, Kansas City, MO, USA
  • Paramdeep S Baweja
    University of Missouri–Kansas City, Kansas City, MO, USA


Sinus of Valsalva aneurysm, aorto–atrial fistula, heart failure


A ruptured sinus of Valsalva aneurysm as a cause of aorto–atrial fistula is very rare. We present the case of a 53-year-old female who presented with symptoms of acute heart failure and suspicion of an aorto–atrial fistula found on a transthoracic echocardiogram, which was confirmed on transesophageal echocardiography. A coronary angiogram showed normal coronary arteries but confirmed the right aorto–atrial fistula on aortogram. She underwent successful surgical repair of the fistula. Her postoperative echocardiogram showed a normal right atrium and right ventricle with no shunt. A ruptured sinus of Valsalva aneurysm is a devastating event and presents as acute heart failure. Prompt diagnosis and surgical repair is necessary to prevent mortality.



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    Published: 2020-03-06
    Issue: 2020: Vol 7 No 4 (view)

    How to cite:
    Ali Z, Asif T, Sheehy J, Jacob D, Baweja PS. Ruptured Sinus of Valsalva Aneurysm Causing Aorto–Atrial Fistula and Acute Heart Failure: A Rare Encounter. EJCRIM 2020;7 doi:10.12890/2020_001499.