Acute Soft Head Syndrome (Subgaleal Haematoma) with Periorbital Oedema as a Rare Presentation in Sickle Cell Disease
  • Rehab Yusuf AL-Ansari
    Adult Hematology Unit, Internal Medicine Department, KFMMC, Dhahran, Kingdom of Saudi Arabia
  • Maan Al Harbi
    Internal Medicine Department, KFMMC, Dhahran, Kingdom of Saudi Arabia
  • Nawaf Al-Jubair
    Neuroradiology unit, Radiology Department, KFMMC, Dhahra, Kingdom of Saudi Arabia
  • Leena Abdalla
    Adult Hematology Unit, Internal Medicine Department, KFMMC, Dhahran, Kingdom of Saudi Arabia

Keywords

Sickle cell, subgaleal hematoma, periorbital edema, soft head syndrome, orbital compression syndrome

Abstract

Background: Sickle cell disease is a genetic condition frequently found in Africa and the Arabian Peninsula. Uncommon complications include subgaleal haematoma (soft head syndrome) and periorbital oedema.
Case presentation: A 17-year-old male patient presented with body aches and progressive right parieto-temporal and frontal head swelling. Physical examination revealed puffiness of the right eye that progressed rapidly to reddish periorbital oedema sparing the extraocular muscle and pupil response to light. CT and MRI of the brain suggested multiple subgaleal haematomas (soft head syndrome) and right periorbital oedema.
Conclusion:Subgaleal haematoma (soft head syndrome) and periorbital oedema are uncommon complications of sickle cell disease. Management is conservative rather than surgical.

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    Published: 2020-07-30
    Issue: 2020: Vol 7 No 10 (view)


    How to cite:
    1.
    AL-Ansari RY, Al Harbi M, Al-Jubair N, Abdalla L. Acute Soft Head Syndrome (Subgaleal Haematoma) with Periorbital Oedema as a Rare Presentation in Sickle Cell Disease. EJCRIM 2020;7 doi:10.12890/2020_001766.

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