A Rare Case of Exocrine Pancreatic Insufficiency
  • Mohamed Labied
    Emergency Radiology Department, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy of Casablanca, Morocco
  • Houria Tabakh
    Emergency Radiology Department, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy of Casablanca, Morocco
  • Hamza Guezri
    Emergency Radiology Department, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy of Casablanca, Morocco
  • Abdellatif Siwane
    Emergency Radiology Department, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy of Casablanca, Morocco
  • Najwa Touil
    Emergency Radiology Department, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy of Casablanca, Morocco
  • Omar Kacimi
    Emergency Radiology Department, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy of Casablanca, Morocco
  • Nabil Chikhaoui
    Emergency Radiology Department, Ibn Rochd University Hospital, Faculty of Medicine and Pharmacy of Casablanca, Morocco

Keywords

Fat, pancreas, lipomatous pseudohypertrophy

Abstract

Lipomatous pseudohypertrophy (LPH) of the pancreas is an uncommon affection of exocrine pancreatic insufficiency. It is defined as substitution of the pancreatic exocrine gland by a large fat component. We report the case of a young patient with malabsorption syndrome (chronic diarrhoea and steatorrhoea), abnormal laboratory results and normal fibroscopy. Computed tomography revealed characteristic diffuse pancreatic abnormalities.

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References

  • Aubert A, Gornet JM, Hammel P, Lévy P, O'Toole D, Ruszniewski P, et al. [Diffuse primary fat replacement of the pancreas: an unusual cause of steatorrhea]. Gastroenterol Clin Biol 2007;31(3):303–306.
  • Durie PR. Pancreatic aspects of cystic fibrosis and other inherited causes of pancreatic dysfunction. Med Clin North Am 2000;84(3):609–620.
  • Nakamura M, Katada N, Sakakibara A, Okumura N, Kato E, Takeichi M, et al. Huge lipomatous pseudohypertrophy of the pancreas. Am J Gastroenterol 1979;72(2):171–174.
  • Danovitch SH, Paley R, Mann O, Choisser R, Bayless T. Vanishing pancreas. Lipomatous infiltration of the pancreas. JAMA 1985;253(10):1442–1443.
  • Smith OP. Shwachman-Diamond syndrome. Semin Hematol 2002;39(2):95–102.
  • Dror Y, Freedman MH. Shwachman-Diamond syndrome. Br J Haematol 2002;118(3):701–713.
  • Maunoury V, Nieuwarts S, Ferri J, Ernst O. Lipomatose pancréatique révélatrice d'un syndrome de Johanson-Blizzard [Pancreatic lipomatosis revealing Johanson-Blizzard syndrome]. Gastroenterol Clin Biol 1999;23(10):1099–1101.
  • Worthen NJ, Beabeau D. Normal pancreatic echogenicity: relation to age and body fat. AJR Am J Roentgenol 1982;139(6):1095–1098.
  • Heuck A, Maubach PA, Reiser M, Feuerbach S, Allgayer B, Lukas P, et al. Age-related morphology of the normal pancreas on computed tomography. Gastrointest Radiol 1987;12(1):18–22.
  • Guermazi A, Benchaib N, Nolen N, Tabti B, Zagdanski AM. Fatty replacement of the pancreas in a patient with asymptomatic pulmonary cystic fibrosis. J Radiol 2003;84(4 Pt 1):409–411.
  • Boglino C, Inserra A, Silvano A, Ciprandi G, Boldrini R, Caione P. Intrapancreatic lipoma: a case report (in Italian). Pediatr Med Chir 1993;15(4):397–399.
  • Ueki T, Mizuno M, Nakagawa M, et al. A case of diffuse fatty replacement of the pancreas which guessed lipomatous pseudohypertrophy of the pancreas (in Japanese). Tan to Sui 2006;27:259–262.

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    Published: 2021-05-18
    Issue: 2021: Vol 8 No 5 (view)

    How to cite:
    1.
    Labied M, Tabakh H, Guezri H, Siwane A, Touil N, Kacimi O, Chikhaoui N. A Rare Case of Exocrine Pancreatic Insufficiency. EJCRIM 2021;8 doi:10.12890/2021_002256.

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