Haemophagocytic Lymphohistiocytosis as a Complication of Israeli Spotted Fever
  • Maria Margarida Andrade
    Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Ana Gorgulho
    Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Rita Tinoco Magalhães
    Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Rita Valadas
    Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Luís Miguel Pereira
    Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Sara Freire
    Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Diogo Cruz
    Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal; Faculty of Medicine, University of Lisbon, Lisbon, Portugal

Keywords

Rickettsiosis, spotted fever, haemophagocytic, purpura fulminans, polyneuropathy

Abstract

Rickettsia spp. human infection is endemic in Portugal in the form of Mediterranean spotted fever caused by R. conorii subsp. conorii and Israeli spotted fever (ISF) caused by R. conorii subsp. israelensis. We describe a rare case of haemophagocytic lymphohistiocytosis (HLH) due to ISF, with atypical manifestations. We highlight the need for clinical suspicion for this diagnosis and the importance of timely intervention and support.

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    Published: 2022-01-17
    Issue: 2022: Vol 9 No 1 (view)


    How to cite:
    1.
    Andrade MM, Gorgulho A, Tinoco Magalhães R, Valadas R, Pereira LM, Freire S, Cruz D. Haemophagocytic Lymphohistiocytosis as a Complication of Israeli Spotted Fever. EJCRIM 2022;9 doi:10.12890/2021_003073.

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