Rhabdomyosarcoma of the nasal cavity: a case report
  • Meiying Huang
    Hezhou People’s Hospital, Hezhou, Guangxi, China
  • Bifan Deng
    Hezhou People’s Hospital, Hezhou, Guangxi, China

Keywords

Rhabdomyosarcoma, endoscopic sinus surgery, acinar

Abstract

Introduction: Rhabdomyosarcoma is a high-grade malignant neoplasm with skeletal muscle differentiation; a common soft tissue sarcoma in children but considered one of the rarest in adults.
Case description: We report a case of 35-year-old male with a chronic productive cough and haemoptysis for five days. A CT scan of the nasopharynx revealed a blocked left maxillary and ethmoid sinus with bone destruction. These findings raised a suspicion of a tumour, and trans-nasal endoscopic sinus surgery was performed.
Discussion: Nasal rhabdomyosarcoma is a rare adult malignant tumour. Most patients have lymphatic metastasis or skull base tumour infiltration at the time of the initial diagnosis and treatment, which poses a challenge to the diagnosis and management.
Conclusion: Nasal acinar rhabdomyosarcoma, one of the histopathological types of rhabdomyosarcoma, has rapid disease progression and high mortality. Therefore, the treatment of rhabdomyosarcoma requires a combination of surgery, chemotherapy, radiotherapy, and immunotherapy to work together to achieve the best care for the patient.

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    Published: 2023-06-14
    Issue: 2023: Vol 10 No 7 (view)


    How to cite:
    1.
    Huang M, Deng B. Rhabdomyosarcoma of the nasal cavity: a case report. EJCRIM 2023;10 doi:10.12890/2023_003926.