Wells syndrome with generalized oedema
  • Magdalini Manti
    First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece
  • Efthymia Pappa
    First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece
  • Vasiliki Arkouli
    First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece
  • Leonidas Marinos
    Department of Hematopathology “Evangelismos” General Hospital, Athens, Greece
  • Constantinos Christopoulos
    First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece

Keywords

Wells syndrome, Churg-Strauss syndrome, eosinophilia, cellulitis, vasculitis

Abstract

Wells syndrome or eosinophilic cellulitis is a rare and relapsing skin disease which lacks systemic involvement. A skin biopsy is needed to establish a diagnosis. Several precipitating factors have been proposed but no proven causative link has been found. On the other hand, Churg-Strauss syndrome, also known as eosinophilic granulomatosis with polyangiitis (EGPA), an auto-immune disease, is associated with multiorgan, including cutaneous manifestations. We report a case with overlapping features of Wells and Churg-Strauss syndrome, suggesting that these syndromes could be part of the same nosological entity.

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    Published: 2023-06-19
    Issue: 2023: Vol 10 No 7 (view)

    How to cite:
    1.
    Manti M, Pappa E, Arkouli V, Marinos L, Christopoulos C. Wells syndrome with generalized oedema. EJCRIM 2023;10 doi:10.12890/2023_003954.

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