Zinner's syndrome and retroperitoneal fibrosis: an unknown association
  • Miguel Morante-Ruiz
    Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Fernando Tornero-Romero
    Autoinmune Disease's Unit, Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Carmelo Palacios-Miras
    Radiology Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Fernado Vicente Lage-Estébanez
    Autoinmune Disease's Unit, Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Lara Cantero-Del Olmo
    Autoinmune Disease's Unit, Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Iris Martínez-Alemany
    Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Juan Martínez-Andrés
    Internal Medicine Department, Hospital de Manisses, Valencia, Spain

Keywords

Zinner’s Syndrome, retroperitoneal fibrosis, rare diseases, renal failure, methotrexate

Abstract

We report the case of a 24-year-old male presenting with obstructive renal failure, characterised by imaging evidence of a cystic lesion contingent upon the seminal vesicle and concurrent renal agenesis. Initial management involved urinary diversion, followed by outpatient monitoring and subsequent recurrence. Subsequent diagnostic assessments led to the identification of Zinner's syndrome, accompanied by retroperitoneal fibrosis. We present the clinical course, diagnostic methodology and the efficacious implementation of medical-surgical therapeutic interventions, yielding favourable outcomes.

VIEW THE ENTIRE ARTICLE

References

  • Zinner A. Einfall von Intravesikaler Samenblasenzyste. Wien Med Wochenschr 1914;64:605–609.
  • Liu T, Li X, Huang L, Li H, Cai K, Jiang J, et al. Zinner syndrome: an updated pooled analysis based on 214 cases from 1999 to 2020: systematic review. Ann Palliat Med 2021;10:2271–2282.
  • van den Ouden D, Blom JH, Bangma C, de Spiegeleer AH. Diagnosis and management of seminal vesicle cysts associated with ipsilateral renal agenesis: a pooled analysis of 52 cases. Eur Urol 1998;33:433–440.
  • Juho Y-C, Wu S-T, Tang S-H, Cha T-L, Meng E. An unexpected clinical feature of Zinner’s Syndrome – a case report. Urol Case Rep 2015;3:149–151.
  • Zhang D-X, Li Y, Li X-G, Zhu X, Teng J-F, Wang K, et al. Transperitoneal laparoscopic excision of primary seminal vesicle benign tumors: surgical techniques and follow-up outcomes. Urology 2013;82:237–241.
  • Views: 307
    HTML downloads: 48
    PDF downloads: 265


    Published: 2024-01-09
    Issue: 2024: Vol 11 No 2 (view)


    How to cite:
    1.
    Morante-Ruiz M, Tornero-Romero F, Palacios-Miras C, Lage-Estébanez FV, Cantero-Del Olmo L, Martínez-Alemany I, Martínez-Andrés J. Zinner’s syndrome and retroperitoneal fibrosis: an unknown association. EJCRIM 2024;11 doi:10.12890/2024_004246.