Zinner's syndrome and retroperitoneal fibrosis: an unknown association
  • Miguel Morante-Ruiz
    Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Fernando Tornero-Romero
    Autoinmune Disease's Unit, Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Carmelo Palacios-Miras
    Radiology Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Fernado Vicente Lage-Estébanez
    Autoinmune Disease's Unit, Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Lara Cantero-Del Olmo
    Autoinmune Disease's Unit, Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Iris Martínez-Alemany
    Internal Medicine Department, Hospital Universitario Fundación Jiménez Díaz, Madrid, Spain
  • Juan Martínez-Andrés
    Internal Medicine Department, Hospital de Manisses, Valencia, Spain

Keywords

Zinner’s Syndrome, retroperitoneal fibrosis, rare diseases, renal failure, methotrexate

Abstract

We report the case of a 24-year-old male presenting with obstructive renal failure, characterised by imaging evidence of a cystic lesion contingent upon the seminal vesicle and concurrent renal agenesis. Initial management involved urinary diversion, followed by outpatient monitoring and subsequent recurrence. Subsequent diagnostic assessments led to the identification of Zinner's syndrome, accompanied by retroperitoneal fibrosis. We present the clinical course, diagnostic methodology and the efficacious implementation of medical-surgical therapeutic interventions, yielding favourable outcomes.

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References

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    Published: 2024-01-09
    Issue: 2024: Vol 11 No 2 (view)

    How to cite:
    1.
    Morante-Ruiz M, Tornero-Romero F, Palacios-Miras C, Lage-Estébanez FV, Cantero-Del Olmo L, Martínez-Alemany I, Martínez-Andrés J. Zinner’s syndrome and retroperitoneal fibrosis: an unknown association. EJCRIM 2024;11 doi:10.12890/2024_004246.