Fuchs Syndrome with Isolated Oral Mucosa Lesions due to Severe Herpes Simplex Cheilitis in a Patient with Idiopathic Thrombocytopenic Purpura
  • Gian-Carlo Eyer
    Thun General Hospital, Thun, Switzerland
  • Kristine Heidemeyer
    Department of Dermatology, Inselspital, Bern University Hospital, University of Bern, Bern, Switzerland
  • Aristomenis Exadakltylos
    Department of Emergency Medicine, Inselspital, University Hospital, University of Bern, Bern, Switzerland
  • Mairi Ziaka
    Thun General Hospital, Thun, Switzerland

Keywords

Fuchs syndrome, herpes simplex cheilitis, idiopathic thrombocytopenic purpura

Abstract

Stevens-Johnson syndrome (SJS) is a severe dermatological disease classically characterized by erythematous target lesions and mucosal involvement. Fuchs syndrome is an incomplete presentation of SJS which has oral, conjunctival and genital manifestations but no skin lesions. To the best of our knowledge, our case of Fuchs syndrome in an 80-year-old man is the first such case related to herpes simplex virus (HSV)-1 infection to be described. Our patient quickly recovered following IVIG therapy, although specific treatment is still a topic of discussion. Research is required on this poorly understood dermatological disease to determine optimum therapy.

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    Published: 2022-04-04
    Issue: 2022: Vol 9 No 4 (view)

    How to cite:
    1.
    Eyer G-C, Heidemeyer K, Exadakltylos A, Ziaka M. Fuchs Syndrome with Isolated Oral Mucosa Lesions due to Severe Herpes Simplex Cheilitis in a Patient with Idiopathic Thrombocytopenic Purpura. EJCRIM 2022;9 doi:10.12890/2021_003278.