Kikuchi-Fujimoto Disease Associated with Sjögren’s Syndrome: A Case Report
  • Abdul-Wahab Al-Allaf
    Rheumatology Department, Hamad Medical Corporation, Doha, Qatar
  • Yousef Yahia
    Hamad Medical Corporation


Kikuchi-Fujimoto disease, Sjögren’s syndrome, necrotizing histiocytic lymphadenitis


Kikuchi-Fujimoto disease (KFD) or Kikuchi histiocytic necrotizing lymphadenitis, is an extremely rare, benign and self-limiting disease which can be confused with lymphoma and sometime with infections such as tuberculosis. It has also been infrequently reported in association with autoimmune diseases. KFD shares sex and age predisposition as well as histological features with systemic lupus erythematosus. The co-existence of KFD with primary Sjögren’s syndrome has only been rarely reported. Here we describe the case of a 33-year-old woman who was diagnosed with KFD and also found to have primary Sjögren’s syndrome.



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    Published: 2018-03-06
    Issue: Vol. 5 No. 5 (view)

    How to cite:
    Al-Allaf A-W, Yahia Y. Kikuchi-Fujimoto Disease Associated with Sjögren’s Syndrome: A Case Report. EJCRIM 2018;5 doi:10.12890/2018_000856.