Pulmonary Arteriovenous Malformation can be Associated with Embolic Stroke of Undetermined Source (ESUS)

  • Mariana Barros Cruz Internal Medicine Service, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal
  • Nuno Palma Internal Medicine Service, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal
  • Joao Rocha Neurology Service, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal
  • Ricardo Meireles Internal Medicine Service, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal

Keywords

Idiopathic pulmonary arteriovenous malformation, embolic stroke, extra-cardiac shunt

Abstract

Pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies. Alternative designations are pulmonary arteriovenous fistulae or aneurysms. Although mostly asymptomatic, PAVMs can cause respiratory symptoms due to right-to-left shunt. The central nervous system is a potential target for complications, including stroke, as a result of paradoxical embolism. In this report, the authors describe an unusual case of cerebral emboli caused by paradoxical embolism through a PAVM, presenting with a broad pathology including orthodeoxia, central cyanosis and digital clubbing, which should be kept in mind since misdiagnosis may cause severe morbidity in young adults.

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  • Published: 2019-11-06

    Issue: LATEST ONLINE (view)

    Section: Articles

    How to cite:
    Cruz, M., Palma, N., Rocha, J., & Meireles, R. (2019). Pulmonary Arteriovenous Malformation can be Associated with Embolic Stroke of Undetermined Source (ESUS). European Journal of Case Reports in Internal Medicine, 2. https://doi.org/https://doi.org/10.12890/2019_001262