Acquired von Willebrand Syndrome and Chronic Anaemia: A Different Diagnostic Approach

  • Nuno Zarcos Palma Serviço de Medicina Interna, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal http://orcid.org/0000-0002-7036-9976
  • Mariana da Cruz Serviço de Medicina Interna, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal
  • Gisela Evaristo Vasconcelos Serviço de Medicina Interna, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal
  • Vitor Fagundes Serviço de Medicina Interna, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal
  • Lindora Pires Serviço de Medicina Interna, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal
  • Mari Mesquita Serviço de Medicina Interna, Centro Hospitalar Tâmega e Sousa, Penafiel, Portugal

Keywords

Heyde’s syndrome, hypertrophic obstructive cardiomyopathy, acquired von Willebrand syndrome, angiodysplasia, anemia

Abstract

Heyde’s syndrome is a form of acquired von Willebrand syndrome that consists of bleeding from intestinal angiodysplasia in the presence of aortic stenosis (AS). An association with obstructive hypertrophic cardiomyopathy, rather than AS, by a similar mechanism has also been described. We report the case of a 78-year-old woman with chronic anaemia and hypertrophic obstructive cardiomyopathy in whom intestinal angiodysplasia with active bleeding was identified by an unconventional method. In this case, the authors describe a different approach to reach the correct diagnosis.

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  • Published: 2019-06-10

    Issue: Vol 6 No 6 (view)

    Section: Articles

    How to cite:
    Zarcos Palma, N., da Cruz, M., Vasconcelos, G., Fagundes, V., Pires, L., & Mesquita, M. (2019). Acquired von Willebrand Syndrome and Chronic Anaemia: A Different Diagnostic Approach. European Journal of Case Reports in Internal Medicine, 6(6). https://doi.org/https://doi.org/10.12890/2019_001137