Refractory Orbital Myositis in Systemic Lupus Erythematosus - A Role for Rituximab
  • Joana Rodrigues Morais
    Internal Medicine Department, Hospital Pedro Hispano, Unidade Local de Saúde de Matosinhos, Portugal https://orcid.org/0000-0003-3717-4488
  • Raquel Rodrigues Santos
    Internal Medicine Department, Hospital Pedro Hispano, Unidade Local de Saúde de Matosinhos, Portugal
  • Paula Pires Costa
    Internal Medicine Service, Hospital do Divino Espírito Santo, Ponta Delgada, Portugal
  • Tomás Fonseca
    Clinical Immunology Unit, Centro Hospitalar Universitário do Porto, Portugal
  • Fátima Farinha
    Clinical Immunology Unit, Centro Hospitalar Universitário do Porto, Portugal

Keywords

Orbital myositis, systemic lupus erythematosus, corticosteroids, rituximab

Abstract

Orbital myositis in systemic lupus erythematosus (SLE) is a rare entity with risk of serious complications. Timely treatment with effective immunosuppressors is desirable.

We report a case of a 32-year-old female patient with SLE who presented with an acute ocular pain and extraorbital muscle thickening, consistent with orbital myositis.

Association with SLE was made after exclusion of other aetiologies. Due to refractoriness to steroids, off-label rituximab was initiated with clinical and imaging parameter improvement.

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    Published: 2021-12-10
    Issue: 2021: Vol 8 No 12 (view)


    How to cite:
    1.
    Rodrigues Morais J, Rodrigues Santos R, Pires Costa P, Fonseca T, Farinha F. Refractory Orbital Myositis in Systemic Lupus Erythematosus - A Role for Rituximab. EJCRIM 2021;8 doi:10.12890/2021_003038.